A case of large vascular plexiform neurofibroma associated with giant café-au-lait patch and scoliosis

Jiehyun Jeon, Jun Ha Park, Dong Soo Yu, Young Chul Kye, Soo Nam Kim

Research output: Contribution to journalArticle

Abstract

Plexiform neurofibromas are benign proliferations arising from the peripheral nerves and represent one of the diagnostic features of neurofibromatosis type 1. We present a case of a 14-year-old boy, who had large vascular neurofibromatous elephantiasis associated with a giant café-au-lait patch on his lateral aspect of the left hemithorax. Although he had no perceptible symptoms, radiologic examination revealed mild thoracic scoliosis with left side convexity. Our treatment of the skin lesion was one-stage palliative tumor debulking.

Original languageEnglish
Pages (from-to)1513-1517
Number of pages5
JournalKorean Journal of Dermatology
Volume43
Issue number11
Publication statusPublished - 2005 Nov 1

Fingerprint

Plexiform Neurofibroma
Elephantiasis
Neurofibromatosis 1
Scoliosis
Peripheral Nerves
Blood Vessels
Thorax
Skin
Neoplasms
Therapeutics

Keywords

  • Giant café-au-lait patch
  • Plexiform neurofibroma
  • Scoliosis

ASJC Scopus subject areas

  • Dermatology

Cite this

A case of large vascular plexiform neurofibroma associated with giant café-au-lait patch and scoliosis. / Jeon, Jiehyun; Park, Jun Ha; Yu, Dong Soo; Kye, Young Chul; Kim, Soo Nam.

In: Korean Journal of Dermatology, Vol. 43, No. 11, 01.11.2005, p. 1513-1517.

Research output: Contribution to journalArticle

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