Abstract
We present here the case of a 33-month-old male patient with Wolf-Hirschhorn syndrome (WHS) and who underwent tympanoplasty and myringotomy. WHS is caused by a rare chromosomal abnormality, which is the deletion of the short arm of chromosome number 4. The typical craniofacial features of WHS patients such as micrognathia, microcephaly and the muscular weakness can make using neuromuscular blocking agents and performing intubation difficult. Moreover, there are a few previous case reports showing that malignant hyperthermia occurred during and after an operation in which the anesthesia was done with inhalation agents, so special anesthetic care is needed when operating on a WHS patient. By carefully intubating the patient and using total intravenous anesthesia, we performed successful anesthesia without any complications. We describe here the anesthetic management of a WHS patient and we review the relevant literature.
| Original language | English |
|---|---|
| Pages (from-to) | 119-123 |
| Number of pages | 5 |
| Journal | Korean Journal of Anesthesiology |
| Volume | 60 |
| Issue number | 2 |
| DOIs | |
| Publication status | Published - 2011 Feb 1 |
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Keywords
- Difficult intubation
- Malignant hyperthermia
- Total intra-venous anesthesia
- Wolf-Hirschhorn syndrome
ASJC Scopus subject areas
- Anesthesiology and Pain Medicine
Cite this
Anesthetic experience using total intra-venous anesthesia for a patient with Wolf-Hirschhorn syndrome - A case report. / Choi, Jae Ho; Kim, Jae Hwan; Park, Young Cheol; Kim, Woon Young; Lee, Yoon Sook.
In: Korean Journal of Anesthesiology, Vol. 60, No. 2, 01.02.2011, p. 119-123.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Anesthetic experience using total intra-venous anesthesia for a patient with Wolf-Hirschhorn syndrome - A case report
AU - Choi, Jae Ho
AU - Kim, Jae Hwan
AU - Park, Young Cheol
AU - Kim, Woon Young
AU - Lee, Yoon Sook
PY - 2011/2/1
Y1 - 2011/2/1
N2 - We present here the case of a 33-month-old male patient with Wolf-Hirschhorn syndrome (WHS) and who underwent tympanoplasty and myringotomy. WHS is caused by a rare chromosomal abnormality, which is the deletion of the short arm of chromosome number 4. The typical craniofacial features of WHS patients such as micrognathia, microcephaly and the muscular weakness can make using neuromuscular blocking agents and performing intubation difficult. Moreover, there are a few previous case reports showing that malignant hyperthermia occurred during and after an operation in which the anesthesia was done with inhalation agents, so special anesthetic care is needed when operating on a WHS patient. By carefully intubating the patient and using total intravenous anesthesia, we performed successful anesthesia without any complications. We describe here the anesthetic management of a WHS patient and we review the relevant literature.
AB - We present here the case of a 33-month-old male patient with Wolf-Hirschhorn syndrome (WHS) and who underwent tympanoplasty and myringotomy. WHS is caused by a rare chromosomal abnormality, which is the deletion of the short arm of chromosome number 4. The typical craniofacial features of WHS patients such as micrognathia, microcephaly and the muscular weakness can make using neuromuscular blocking agents and performing intubation difficult. Moreover, there are a few previous case reports showing that malignant hyperthermia occurred during and after an operation in which the anesthesia was done with inhalation agents, so special anesthetic care is needed when operating on a WHS patient. By carefully intubating the patient and using total intravenous anesthesia, we performed successful anesthesia without any complications. We describe here the anesthetic management of a WHS patient and we review the relevant literature.
KW - Difficult intubation
KW - Malignant hyperthermia
KW - Total intra-venous anesthesia
KW - Wolf-Hirschhorn syndrome
UR - http://www.scopus.com/inward/record.url?scp=79952570352&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=79952570352&partnerID=8YFLogxK
U2 - 10.4097/kjae.2011.60.2.119
DO - 10.4097/kjae.2011.60.2.119
M3 - Article
VL - 60
SP - 119
EP - 123
JO - Korean Journal of Anesthesiology
JF - Korean Journal of Anesthesiology
SN - 2005-6419
IS - 2
ER -