Caroli's disease misdiagnosed as intraductal papillary neoplasm of the bile duct

Dae Hoe Gu, Min Seon Park, Chang Ho Jung, Yang Jae Yoo, Jae Young Cho, Yun Ho Lee, Yeon Seok Seo, Hyung Joon Yim, Soon-Ho Um, Ho Sang Ryu

Research output: Contribution to journalArticle

8 Citations (Scopus)


Caroli's disease is a rare autosomal-recessive disorder caused by malformation of the ductal plate during embryonic development. Although it is present at birth, Caroli's disease is typically not diagnosed until between the second and fourth decades of life, as it was in the present patient. Here we report a rare case of Caroli's disease limited to one liver segment, which was initially misdiagnosed as an intraductal papillary neoplasm of the bile duct. The asymptomatic patient was treated with liver segmentectomy.

Original languageEnglish
Pages (from-to)175-179
Number of pages5
JournalClinical and molecular hepatology
Issue number2
Publication statusPublished - 2015 Jun 1



  • Caroli's disease
  • Intraductal papillary neoplasm of the bile duct
  • Segmentectomy

ASJC Scopus subject areas

  • Hepatology
  • Molecular Biology

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