Cochlear implantation in superficial siderosis

Chong Sun Kim, Jae-Jun Song, Min Hyun Park, Young Ho Kim, Ja Won Koo

Research output: Contribution to journalArticle

22 Citations (Scopus)

Abstract

Superficial siderosis (SS) of the central nervous system has been thought to be a rare condition that generates progressive hearing loss, ataxia, pyramidal signs, and dementia. The main cause of hearing loss by SS is thought to be neuronal. Because there is no histopathologic report of the human temporal bone in SS, there is a debate about the possibility of cochlear involvement. We present a 25-year-old man who was investigated for bilateral progressive sensorineural hearing loss and vestibular failure after head trauma. On brain MRI, SS of the central nervous system was detected. Distortion product otoacoustic emission (DPOAE) and auditory brainstem response (ABR) showed no response on both sides. However, integrity of the eighth nerve was proved by the electrical ABR test on the right side and the patient benefited significantly from cochlear implantation. The sensorineural hearing loss in SS seems to be related to cochlear damage as well as neuronal damage. So, cochlear implantation would be a hearing rehabilitation modality for the sensorineural hearing loss caused by SS.

Original languageEnglish
Pages (from-to)892-896
Number of pages5
JournalActa Oto-Laryngologica
Volume126
Issue number8
DOIs
Publication statusPublished - 2006 Aug 1
Externally publishedYes

Fingerprint

Siderosis
Cochlear Implantation
Sensorineural Hearing Loss
Brain Stem Auditory Evoked Potentials
Cochlea
Hearing Loss
Central Nervous System
Temporal Bone
Patient Rights
Ataxia
Craniocerebral Trauma
Hearing
Dementia
Rehabilitation
Brain

Keywords

  • Cochlear implantation
  • Hearing loss
  • Siderosis

ASJC Scopus subject areas

  • Otorhinolaryngology

Cite this

Cochlear implantation in superficial siderosis. / Kim, Chong Sun; Song, Jae-Jun; Park, Min Hyun; Ho Kim, Young; Koo, Ja Won.

In: Acta Oto-Laryngologica, Vol. 126, No. 8, 01.08.2006, p. 892-896.

Research output: Contribution to journalArticle

Kim, CS, Song, J-J, Park, MH, Ho Kim, Y & Koo, JW 2006, 'Cochlear implantation in superficial siderosis', Acta Oto-Laryngologica, vol. 126, no. 8, pp. 892-896. https://doi.org/10.1080/00016480500529330
Kim, Chong Sun ; Song, Jae-Jun ; Park, Min Hyun ; Ho Kim, Young ; Koo, Ja Won. / Cochlear implantation in superficial siderosis. In: Acta Oto-Laryngologica. 2006 ; Vol. 126, No. 8. pp. 892-896.
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