Diagnosis and treatment of cystic lung disease

Sanghoon Park, Eun Joo Lee

Research output: Contribution to journalReview article

4 Citations (Scopus)

Abstract

Cystic lung disease (CLD) is a group of lung disorders characterized by the presence of multiple cysts, defined as air-filled lucencies or low-attenuating areas, bordered by a thin wall (usually < 2 mm). The recognition of CLDs has increased with the widespread use of computed tomography. This article addresses the mechanisms of cyst formation and the diagnostic approaches to CLDs. A number of assessment methods that can be used to confirm CLDs are discussed, including high-resolution computed tomography, pathologic approaches, and genetic/ serologic markers, together with treatment modalities, including new therapeutic drugs currently being evaluated. The CLDs covered by this review are lymphangioleiomyomatosis, pulmonary Langerhans cell histiocytosis, Birt-Hogg-Dube syndrome, lymphocytic interstitial pneumonia/follicular bronchiolitis, and amyloidosis.

Original languageEnglish
Pages (from-to)229-238
Number of pages10
JournalKorean Journal of Internal Medicine
Volume32
Issue number2
DOIs
Publication statusPublished - 2017 Jan 1

Fingerprint

Cysts
Birt-Hogg-Dube Syndrome
Tomography
Lymphangioleiomyomatosis
Lung
Langerhans Cell Histiocytosis
Bronchiolitis
Interstitial Lung Diseases
Amyloidosis
Genetic Markers
Air
Pharmaceutical Preparations
Cystic Disease Of Lung
Therapeutics

Keywords

  • Birt-Hogg-Dube syndrome
  • Cystic lung disease
  • Histiocytosis
  • Lang-erhans-cell
  • Lymphangioleiomyomatosis

ASJC Scopus subject areas

  • Internal Medicine

Cite this

Diagnosis and treatment of cystic lung disease. / Park, Sanghoon; Lee, Eun Joo.

In: Korean Journal of Internal Medicine, Vol. 32, No. 2, 01.01.2017, p. 229-238.

Research output: Contribution to journalReview article

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