Moyamoya disease in a child with previous acute necrotizing encephalopathy

Taik Kun Kim, Baik Lin Eun, Sang Hoon Cha, Kyoo Byung Chung, Jung Hyuck Kim, Baek Hyun Kim, Hwan Hoon Chung

Research output: Contribution to journalArticlepeer-review

5 Citations (Scopus)


A previously healthy 24-day-old boy presented with a 2-day history of fever and had a convulsion on the day of admission. MRI showed abnormal signal in the thalami, caudate nuclei and central white matter. Acute necrotising encephalopathy was diagnosed, other causes having been excluded after biochemical and haematological analysis of blood, urine and CSF. He recovered, but with spastic quadriparesis. At the age of 28 months, he suffered sudden deterioration of consciousness and motor weakness of his right limbs. MRI was consistent with an acute cerebrovascular accident. Angiography showed bilateral middle cerebral artery stenosis or frank occlusion with numerous lenticulostriate collateral vessels consistent with moyamoya disease.

Original languageEnglish
Pages (from-to)644-647
Number of pages4
JournalPediatric Radiology
Issue number9
Publication statusPublished - 2003 Sep 1


  • Acute necrotising encephalopathy
  • Brain moyamoya
  • Child
  • Head
  • MRI

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Radiology Nuclear Medicine and imaging

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