Scleroderma associated with ANCA-associated vasculitis

Hee Rho Young, Jae Choi Seong, Young Ho Lee, Jong Dae Ji, Gwan Gyu Song

Research output: Contribution to journalArticle

10 Citations (Scopus)

Abstract

Scleroderma and ANCA-associated vasculitides (AAV), such as microscopic polyangiitis, are distinct disease entities, but are rarely known to coexist with each other. We have reported on two cases of scleroderma patients for the first time in Korea, and these patients were initially known to have only limited type scleroderma with pulmonary fibrosis, but eventually they were found to be ANCA-positive with the associated clinical features of vasculitis. Both were treated with high-dose steroids and cyclophosphamide and remitted without major sequelae. When scleroderma patients exhibit atypical features such as normotensive renal failure with signs of active inflammation, the possibility of AAV should always be considered.

Original languageEnglish
Pages (from-to)465-468
Number of pages4
JournalRheumatology International
Volume26
Issue number5
DOIs
Publication statusPublished - 2006 Mar 1

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Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis
Limited Scleroderma
Microscopic Polyangiitis
Antineutrophil Cytoplasmic Antibodies
Pulmonary Fibrosis
Korea
Vasculitis
Cyclophosphamide
Renal Insufficiency
Steroids
Inflammation

Keywords

  • ANCA
  • Scleroderma
  • Vasculitis

ASJC Scopus subject areas

  • Rheumatology
  • Immunology and Allergy
  • Immunology

Cite this

Scleroderma associated with ANCA-associated vasculitis. / Young, Hee Rho; Seong, Jae Choi; Lee, Young Ho; Ji, Jong Dae; Song, Gwan Gyu.

In: Rheumatology International, Vol. 26, No. 5, 01.03.2006, p. 465-468.

Research output: Contribution to journalArticle

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