Scleroderma associated with ANCA-associated vasculitis

Hee Rho Young, Jae Choi Seong, Ho Lee Young, Dae Ji Jong, Gwan Gyu Song

    Research output: Contribution to journalArticlepeer-review

    10 Citations (Scopus)


    Scleroderma and ANCA-associated vasculitides (AAV), such as microscopic polyangiitis, are distinct disease entities, but are rarely known to coexist with each other. We have reported on two cases of scleroderma patients for the first time in Korea, and these patients were initially known to have only limited type scleroderma with pulmonary fibrosis, but eventually they were found to be ANCA-positive with the associated clinical features of vasculitis. Both were treated with high-dose steroids and cyclophosphamide and remitted without major sequelae. When scleroderma patients exhibit atypical features such as normotensive renal failure with signs of active inflammation, the possibility of AAV should always be considered.

    Original languageEnglish
    Pages (from-to)465-468
    Number of pages4
    JournalRheumatology International
    Issue number5
    Publication statusPublished - 2006 Mar


    • ANCA
    • Scleroderma
    • Vasculitis

    ASJC Scopus subject areas

    • Rheumatology
    • Immunology and Allergy
    • Immunology


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