Spontaneous rupture of renal angiomyolipoma in a female tuberous sclerosis patient with pulmonary lymphangioleiomyomatosis

Jong Wook Kim, Tae Won Lee, Myung Joon Kim, Mi Mi Oh, Jae Hyun Bae, Hong Seok Park, Je Jong Kim, Kang Soo Shim

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Pulmonary lymphangioleiomyomatosis (LAM) is uncommon debilitating disease, predominantly affecting women of childbearing age. Renal angiomyolipoma (AML) is the most common renal lesion in patients with tuberous sclerosis (TS), but, even without TS, is reported in up to 60% of the patients with LAM, which is frequently diagnosed several years before the LAM itself. However, it is extremely rare for renal AML and pulmonary LAM to simultaneously present in tuberous sclerosis complex. Herein, a case of spontaneous rupture of a renal AML, accompanie by pulmonary LAM, in a reproductive female with TS, managed by selective transcatheter arterial embolization (TAE), is reported.

Original languageEnglish
Pages (from-to)344-347
Number of pages4
JournalKorean Journal of Urology
Volume48
Issue number3
DOIs
Publication statusPublished - 2007 Mar

Keywords

  • Angiomyolipoma
  • Lymphangioleiomyomatosis
  • Tuberous sclerosis

ASJC Scopus subject areas

  • Urology

Fingerprint Dive into the research topics of 'Spontaneous rupture of renal angiomyolipoma in a female tuberous sclerosis patient with pulmonary lymphangioleiomyomatosis'. Together they form a unique fingerprint.

  • Cite this